Priapism in Children with Sickle Cell Disease: Description of a Series 28 Cases at CHU Conakry

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Introduction: the objective of this study was to describe the epidemiological, clinical, therapeutic and evolutionary aspects of priapism in children with sickle cell disease. Methodology: this was a descriptive retrospective study, lasting 6 years from January 1,2017 to December 31, 2022, carried out at the pediatric surgery unit of the Ignace Deen national hospital and at the SOS center drepa of morykanteyah. Itcovered 28 records of sickle cell patients aged 0 to 15 years. Results: we recorded 28 cases of priapism out of 1050 sickle cell patients, a frequency of 2.66%. The average age of patients was 9.79 years with the extremes of 5 and 14 years, 54% of cases were homogygous, pain and rigidity of the penis were the most frequent clinical signs, i e 100%. The duration of symptom evolution was greater than 36 hours in 53.57%. It was an acute priapism in 54% with a nocturnal occurrence in 57%. 39.29% had suffered 1 to 2 episodes of priapism in their history. The medical treatment involved analgesics, rehydration and oral etilefrine in 85.71%, 32.14% and 21.43% respectively. Intracavernous injection of etilefrine was the most used method with 35.71% success rate, while bilateral incision of the corpora cavernosa (distal Al-Ghorab shunt) was the ultimate remedy with 100% success rate. hit. Detumescence was obtained the same day in 60.71%. Fibrosis of the corpora cavernosa and relapse were the complications found. Conclusion: priapism in children with sickle cell disease is a relatively frequent urological emergency, early consultation and adequate care could reduce complications.

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